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      Primary renal angiosarcoma: a diagnostic and therapeutic challenge

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          Abstract

          Primary renal angiosarcoma is an exceedingly rare and aggressive neoplasm. Although it may occur in youth, this tumour is frequently reported in the sixth and seventh decades of life. The clinical presentation is frequently varied. Pathogenesis remains largely unknown and it has overlapping features with other tumours of the kidney. Current treatment options include variable combinations of surgery, chemotherapy and radiotherapy. Reports regarding the disease prognosis and natural history are limited. In this article, we chronicle the case of a patient with primary renal angiosarcoma presenting at an advanced stage as a widely metastasised tumour. Additionally, we undertake here a brief literature review highlighting the rarity and aggressiveness of this condition, its poor prognosis, and the lack of specific management guidelines.

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          Author and article information

          Journal
          BMJ Case Rep
          BMJ Case Rep
          casereports
          bmjcasereports
          BMJ Case Reports
          BMJ Publishing Group (BMA House, Tavistock Square, London, WC1H 9JR )
          1757-790X
          2018
          21 September 2018
          : 2018
          Affiliations
          [1 ] University of Nebraska Medical Center , Omaha, Nebraska, USA
          [2 ] Allama Iqbal Medical College , Lahore, Pakistan
          [3 ] Services Institute of Medical Sciences , Lahore, Punjab, Pakistan
          [4 ] SUNY Downstate Medical Center , Brooklyn, New York, USA
          Author notes
          [Correspondence to ] Dr Faisal Inayat, faisalinayat@ 123456hotmail.com
          Article
          PMC6157581 PMC6157581 6157581 bcr-2018-225484
          10.1136/bcr-2018-225484
          6157581
          30244222
          © BMJ Publishing Group Limited 2018. No commercial re-use. See rights and permissions. Published by BMJ.
          Categories
          Rare Disease
          1523
          Case Report

          urological cancer, oncology

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