a clinical study of patients with ocular adnexal Kaposi's sarcoma was undertaken to study its clinical characteristics. A review of all patients with biopsy confirmed ocular adnexal Kaposi's sarcoma seen between 1962 and 1991. There were eleven patients during this period with the incidence of 1.25 for 10,000 cases. Ages ranged from one to 47 years (average, 33 years). There were 6 males and 5 females. One (9%) patient was seen during the period of 1961 and 1981 and 10 (91%)during the period 1982 and 1991. Of the 10 patients, 9 had ocular Kaposi's sarcoma lesions related to acquires immunodeficiency syndrome. Lesions involved the right and the left eyes in 50% of cases. Localization of lesions was palpebral in 9 (82%) patients and conjunctival in 2 (18%) patients. The clinical appearance was tumoral, modular, polypoid and as subconjunctival hemorrhage. Three patients underwent excision of tumor. The recurrence was of 100% in approximately three weeks of time. All patients infected with HIV died. Ocular Kaposi's sarcoma was not common and its presence is related in most of cases to HIV infection and could be the first manifestation of HIV infection.