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      Double aortic arch anomalies in Children: A Systematic 20-Year Single Center Study.

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          Abstract

          Aortic arch anomalies underlie numerous congenital disorders. Effectively diagnosing and treating them requires close understanding of cardiovascular embryology. As our Center serves the entire pediatric population of our country, we performed a comprehensive retrospective analysis of all aortic arch anomalies diagnosed at our Center over the past 20 years. We analyzed 40 children with aortic arch anomalies, distinguishing two defect types: Group 1 displayed ring-forming anomalies, and Group 2 other types of aortic arch anomalies that did not form a vascular ring. We performed detailed morphological analyses using echocardiography, angiography, computed tomography, or magnetic resonance imaging and generated a catalog of all aortic arch anomalies present. Group 1 was represented by 25 patients; 40% with persistent both aortic arches, and 60% with various forms of right aortic arch and an incomplete left aortic arch. Group 2 was represented by 15 patients with complex heart defects. On the basis of our dataset, the incidence of all aortic arch anomalies was 0.033%, and of ring-forming pathologies 0.021%. Although aortic arch anomalies are rare, it is important to diagnose them correctly. It is critical to distinguish ring-forming types. Although in complex defects the aortic arch anomaly represents only an additive diagnosis, its correct definition could be crucial for further management. Cumulatively, this unique, long-term study provides a systematic patient registry and offers critical epidemiological data to aid the study of rare congenital cardiovascular defects. Clin. Anat. 30:929-939, 2017. © 2017 Wiley Periodicals, Inc.

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          Author and article information

          Journal
          Clin Anat
          Clinical anatomy (New York, N.Y.)
          Wiley
          1098-2353
          0897-3806
          Oct 2017
          : 30
          : 7
          Affiliations
          [1 ] National Institute of Cardiovascular Diseases-Children's Cardiac Center, Limbova Street 1, Bratislava, 833 51, Slovakia.
          [2 ] Department of Cardiology and Angiology, Slovak Medical University and National Institute of Cardiovascular Diseases, Pod Krasnou horkou Street 1, Bratislava, 833 48, Slovakia.
          [3 ] Institute of Histology and Embryology, Faculty of Medicine, Comenius University in Bratislava, Sasinkova Street 4, Bratislava, 811 08, Slovakia.
          [4 ] Department of Radiology, Children's University Hospital, Limbova Street 1, Bratislava, 833 40, Slovakia.
          Article
          10.1002/ca.22955
          28726262
          56096a83-629b-4071-a5ae-5c0272919b8c
          © 2017 Wiley Periodicals, Inc.
          History

          double aortic arch,embryology,right aortic arch,stridor,swallowing disorders,vascular ring

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