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      La dysplasie fibreuse ou maladie de Jaffe-Lichtenstein de la clavicule: à propos d'un cas Translated title: Fibrous dysplasia or Jaffe-Lichtenstein disease of the clavicle: report of a case

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          Abstract

          La dysplasie fibreuse est une maladie osseuse rare, elle représente environ 2,5% des maladies osseuses et 7% des tumeurs osseuses. Nous rapportons le cas d'un enfant âgé de 10 ans, admis pour prise en charge d'une tuméfaction sus claviculaire droite évoluant dans un contexte de conservation de l’état général et chez qui le bilan para clinique a été en faveur de la dysplasie fibreuse de la clavicule.

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          Most cited references11

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          [Craniofacial fibrous dysplasia: a case report].

          Fibrous dysplasia is classified among benign bone tumors. It is a bone development anomaly characterized by hamartoma proliferation of fibrous tissue within the medullary bone, with secondary bony metaplasia, producing immature, newly formed and weakly calcified bone, without maturation of the osteoblast. It can be monostotic or polyostotic. The craniofacial localization occurs in 10%-25% of cases in monostotic forms and in 50% of cases in polyostotic forms. Fibrous dysplasia essentially affects children and young adults, with no sex preference. Its diagnosis is not always straightforward because the functional symptomology is often absent or not specific. Medical imagery is necessary and in difficult cases a bone biopsy. The major complication of the illness remains sarcomatous degeneration. Only symptomatic forms are treated. We report an observation of craniofacial fibrous dysplasia affecting a child and discovery of proptosis, with no other ocular or general functional signs.
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            Symptomatic polyostotic fibrous dysplasia of the thoracic spine.

            We present a case of polyostotic fibrous dysplasia with limited involvement in thoracic spine and adjacent ribs. The patient underwent posterior instrumentation performed between Th3 and Th11 with pedicle screw system, followed by costotransversectomy of 7th and 8th costovertebral junctions and posterior spinal fusion for costal lesions. In the same operation, curettage was done for the lesion in Th6 vertebra and bone grafting and anterior total corpectomy were performed for Th7 and Th8 vertebrae. 360 degrees spinal fusion was done using titanium mesh as strut graft and autogenous rib grafts. Fibrous dysplasia occurs rarely in axial bones than peripheral bones. The cystic lesions in segments of the whole spine should be evaluated for the possibility of fibrous dysplasia with detailed radiographical examination and biopsy.
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              Dysplasie fibreuse

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                Author and article information

                Journal
                Pan Afr Med J
                Pan Afr Med J
                PAMJ
                The Pan African Medical Journal
                The African Field Epidemiology Network
                1937-8688
                05 June 2012
                2012
                : 12
                : 22
                Affiliations
                [1 ]Service de traumatologie orthopédie pédiatrique, CHU Hassan II, Fès, Maroc
                Author notes
                [& ]Corresponding author: Karima Atarraf, Service de traumatologie orthopédie pédiatrique, CHU Hassan II, Fès, Maroc
                Article
                PAMJ-12-22
                3415043
                22891080
                5824f563-0758-4b6a-af1d-4f954016891c
                © Main Karima Atarraf et al.

                The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

                History
                : 26 September 2011
                : 08 February 2012
                Categories
                Case Report

                Medicine
                dysplasie fibreuse,clavicule,enfant,jaffe-lichtenstein
                Medicine
                dysplasie fibreuse, clavicule, enfant, jaffe-lichtenstein

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