Isolated Left Ventricular Noncompaction: An Unclassified Cardiomyopathy with Severe Prognosis in Adults

Abstract

Noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy, which appears to represent an arrest in intrauterine endomyocardial morphogenesis. It is diagnosed both in children and adults. Its common presentation involves heart failure symptoms, ventricular tachyarrhythmias and thromboembolic events, but the age of onset varies widely. The diagnosis is made by the combined appearance of numerous, excessively prominent trabeculations and multiple deep intertrabecular recesses perfused from the ventricular cavity, commonly involving the apical and midventricular segments of the left ventricle. Although the peculiar echocardiographic picture may possibly lead to the correct diagnosis, this condition may be often misdiagnosed or unrecognized since it is not widely known.

Journal

Journal ID (publisher-id): CRD

Journal ID (nlm-ta): Cardiology

Journal ID (doi): 10.1159/issn.0008-6312

Title: Cardiology

Publisher: S. Karger AG

ISSN (Print): 0008-6312

ISSN (Electronic): 1421-9751

Publication date Subscription-year: 2002

Publication date (Print): September 2002

Publication date (Electronic): 26 September 2002

Volume: 98

Issue: 1-2

Pages: 25-32

Affiliations

Departments of ^aCardiology and ^bRadiology, University of Athens, Greece

Article

Publisher ID: 64677 Other ID: Cardiology 2002;98:25–32

DOI: 10.1159/000064677

PubMed ID: 12373044

Copyright statement: © 2002 S. Karger AG, Basel

License:

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Page count

Figures: 4, Tables: 1, References: 46, Pages: 8

Product

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Categories

Subject: General Cardiology