79
views
0
recommends
+1 Recommend
1 collections
    0
    shares
      • Record: found
      • Abstract: found
      • Article: found
      Is Open Access

      Xantogranuloma juvenil del adulto: Reporte de un caso clínico y revisión de la literatura Translated title: Juvenile xanthogranuloma in adult: A case report and review

      review-article

      Read this article at

      Bookmark
          There is no author summary for this article yet. Authors can add summaries to their articles on ScienceOpen to make them more accessible to a non-specialist audience.

          Abstract

          El xantoganuloma juvenil es una enfermedad benigna, poco frecuente en el adulto, forma parte del grupo de las histiocitosis de células no Langerhans, representando el 90 % de las mismas y el 15 % de éstas, se presentan en el adulto. El compromiso de otros órganos es excepcional. La evolución suele ser benigna con autoresolución de las lesiones. Presentamos el caso de una paciente de sexo femenino de 27 años de edad, que presentaba lesiones papulares de 15 días de evolución, en zona periocular, asintomáticas, las que fueron biopsiadas con diagnóstico histopatológico de xantogranuloma juvenil.

          Translated abstract

          Juvenile Xanthogranuloma (JX) is an uncommon benign disease in adults, is part of the group of non-Langerhans cells histiocytosis, representing 90 % of them and 15% of these occur in adults. The involvement of other organs is exceptional. The evolution is usually benign with resolution of disease. We present a case of a female patient of 27 years who had papules with 15 days of evolution, in periocular area, asymptomatic, which were biopsied with histopathologic diagnosis of juvenile xanthogranuloma.

          Related collections

          Most cited references12

          • Record: found
          • Abstract: found
          • Article: not found

          Juvenile xanthogranuloma.

          Juvenile xanthogranuloma (JXG) is a benign, self-healing disorder characterized by solitary or multiple yellow-red nodules on the skin and, occasionally, in other organs. It is predominantly a disease of infancy or early childhood, although adults may also be affected. Histologically, JXG represents an accumulation of histiocytes lacking Birbeck granules (non-Langerhans cells), which can be differentiated from Langerhans cells by specific staining techniques. Affected persons have normal lipid metabolism. JXG is therefore classified as a normolipemic non-Langerhans cell histiocytosis. The patient's general health is not impaired and, in the absence of associated conditions, the prognosis is excellent. Diagnosis is readily made in typical cases, but may be more difficult in unusual variants.
            Bookmark
            • Record: found
            • Abstract: not found
            • Article: not found

            Concurrent development of eruptive xanthogranulomas and hematologic malignancy: two case reports.

              Bookmark
              • Record: found
              • Abstract: found
              • Article: not found

              Adult Xanthogranuloma, Reticulohistiocytosis, and Rosai-Dorfman Disease.

              Adult xanthogranuloma presents most commonly as an orange-tan firm solitary nodule with no systemic manifestations. Recently, some cases have been reported in conjunction with lymphoproliferative disorders. Adult reticulohistiocytosis classically presents as red to yellow-red dermal nodules. In the multicentric form, lesions have a predilection for hands and elbows, with a classic coral bead periungual presentation, and are often associated with symmetric erosive arthritis, particularly of the hands and wrists. The presentation and course of Rosai-Dorfman disease, or sinus histiocytosis with massive lymphadenopathy, can vary. The classic presentation is extensive, painless bilateral cervical lymphadenopathy, but some cases have been entirely extranodal.
                Bookmark

                Author and article information

                Contributors
                Role: ND
                Role: ND
                Role: ND
                Role: ND
                Role: ND
                Journal
                rad
                Revista argentina de dermatología
                Rev. argent. dermatol.
                Asociación Argentina de Dermatología (Ciudad Autónoma de Buenos Aires, , Argentina )
                1851-300X
                June 2016
                : 97
                : 2
                : 64-73
                Affiliations
                [03] orgnameHospital Privado de Córdoba orgdiv1Servicio de Patología
                [01] orgnameHospital Privado de Córdoba orgdiv1Servicio de Dermatología
                [02] orgnameUniversidad Católica de Córdoba orgdiv1Carrera de Posgrado en Dermatología
                Article
                S1851-300X2016000200010
                c8f71258-736d-4c7e-9270-b0bb6a09d7ad

                This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

                History
                : 06 March 2016
                : 01 June 2016
                Page count
                Figures: 0, Tables: 0, Equations: 0, References: 12, Pages: 10
                Product

                SciELO Argentina


                Xantogranuloma juvenil del adulto,Juvenile xanthogranuloma,Xanthogranuloma adult,Xantogranuloma juvenil,Xantogranuloma del adulto,Juvenile xanthogranuloma adult

                Comments

                Comment on this article