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      Fatal cutaneous necrosis mimicking calciphylaxis in a patient with type 1 primary hyperoxaluria.

      1 , , , ,
      Archives of dermatology

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          Abstract

          Cutaneous necrosis of the proximal lower extremities in a patient with end-stage renal disease is the classic presentation of calciphylaxis, an untreatable, rare, generally fatal necrotizing cutaneous syndrome. Type 1 primary hyperoxaluria (PH-1) usually presents in childhood with recurrent urolithiasis. Since enzymatic studies to confirm the metabolic defect are now available, some cases of idiopathic renal failure in adulthood have been shown to be caused by PH-1. These patients may develop vascular oxalate deposits resulting in livedo reticularis and distal acral vascular insufficiency.

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          Author and article information

          Journal
          Arch Dermatol
          Archives of dermatology
          0003-987X
          0003-987X
          Jul 1995
          : 131
          : 7
          Affiliations
          [1 ] Department of Dermatology, Case Western Reserve University, Cleveland, Ohio, USA.
          Article
          7611799
          ce513a78-4bea-445f-a830-10c1f7c79072
          History

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