Renal pseudotumor simulating malignancy in a patient with Adamantiades-Behçet's disease: case report and review of the literature.

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Abstract

Adamantiades-Behçet's disease is a multisystem recurrent syndrome with vasculitis being the underlying histopathological lesion. We report on a patient with Behçet's disease who developed a renal mass raising the suspicion of a malignant neoplasm. The pathologic examination revealed an inflammatory pseudotumor. The concurrent presentation of these two entities seems to be more than coincidental.

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End-Stage Renal Failure due to Crescentic Glomerulonephritis in a Patient with Behçet’s Syndrome

Takanobu Sakemi, Tomiyoshi Yoshiyuki, Yuji Ikeda … (1998)

We report a rare case of a patient with Behçet’s syndrome who developed end-stage renal failure due to crescentic glomerulonephritis (GN). A 20-year-old male patient had suffered from uveitis, aphthous mouth ulcers and genital ulceration for the past 7 years. His renal function rapidly deteriorated and renal biopsy specimens obtained when his serum creatinine level was 3 mg/dl showed diffuse proliferative GN with fibrous crescent formation in 75% of glomeruli excluding totally sclerotic glomeruli. Immune complexes were identified by demonstration of complement and immunoglobulins in the glomeruli. He developed end-stage renal failure during a 1-year course and received maintenance hemodialysis. We reviewed the literature on severe forms of GN in patients with Behçet’s syndrome.