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      Paniculitis en paciente con dermatomiositis Translated title: Panniculitis in a patient with dermatomyositis

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          Abstract

          La paniculitis es una manifestación cutánea infrecuente de la dermatomiositis. Puede preceder hasta en 14 meses a otras manifestaciones de la dermatomiositis. En todos los casos, la miositis y la paniculitis presentan mejoría simultánea durante el tratamiento. Describimos una paciente de sexo femenino de 30 años que presenta lesiones clínica e histológicamente compatibles con paniculitis luego de 2 meses de que el compromiso muscular y cutáneo permitió el diagnóstico de dermatomiositis. Las lesiones cutáneas remitieron con el tratamiento esteroideo.

          Translated abstract

          Panniculitis is a rarely reported clinical finding in dermatomyositis. It may precede the other manifestations associated with dermatomyositis by as much as 14 months. In all cases, myositis and panniculitis improve simultaneously during treatment. The present report describes the case of a 30-year-old female patient with clinical and histopathological findings consistent with panniculitis two months after the onset of the muscle and cutaneous symptoms that permitted diagnosis of dermatomyositis. The skin lesions regressed following steroid treatment.

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          Dermatomyositis: cutaneous manifestations of its variants.

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            Dermatomyositis treated with high-dose intravenous immunoglobulins and associated with panniculitis.

            Polymyositis and dermatomyositis are idiopathic inflammatory myopathies characterized by subacute symmetrical weakness of proximal limb and trunk muscles. Dermatomyositis is distinguished from polymyositis by the presence of rash. We describe an adult patient with treatment-resistant childhood-type dermatomyositis who made a good response to high dose intravenous immunoglobulins. Additionally, there was evidence of panniculitis which is an unusual histopathological finding in dermatomyositis.
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              Panniculitis in juvenile dermatomyositis

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                Author and article information

                Contributors
                Role: ND
                Role: ND
                Role: ND
                Role: ND
                Role: ND
                Journal
                abd
                Anais Brasileiros de Dermatologia
                An. Bras. Dermatol.
                Sociedade Brasileira de Dermatologia (Rio de Janeiro )
                1806-4841
                February 2011
                : 86
                : 1
                : 146-148
                Affiliations
                [1 ] Hospital General de Agudos Dr. C. Argerich Argentina
                Article
                S0365-05962011000100023
                10.1590/S0365-05962011000100023
                5ec99a36-cd9a-4bf3-805b-783ca949efe9

                http://creativecommons.org/licenses/by/4.0/

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                SciELO Brazil

                Self URI (journal page): http://www.scielo.br/scielo.php?script=sci_serial&pid=0365-0596&lng=en
                Categories
                DERMATOLOGY

                Dermatology
                Dermatomyositis,Panniculitis,Steroids,Dermatomiositis,Esteroides,Paniculitis
                Dermatology
                Dermatomyositis, Panniculitis, Steroids, Dermatomiositis, Esteroides, Paniculitis

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