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      Síndrome de Aicardi: relato de caso Translated title: Aicardi syndrome: case report

      case-report

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          Abstract

          Relatamos um caso de síndrome de Aicardi completa em criança do sexo feminino de 2 meses de idade com defeitos lacunares da coróide, espasmos em flexão, agenesia de corpo caloso e alterações eletrencefalográficas do tipo hipsarritmia assimétrica e alterna atendida no Serviço de Neuropediatria e Neurofisiologia clínica do Hospital de Base de São José do Rio Preto, SP .

          Translated abstract

          We report a case of Aicardi syndrome in a female child with 2 month old, ocular abnormalities "chorioretinal lacunae", flexion in spasms, hipsarrhythmic "split brain", callosal agenesis refered to Service of Neuropediatric and Neurophysiology of Base Hospital of São José do Rio Preto, SP, Brazil.

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          Most cited references11

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          A new syndrome spasm in flexion, callosal agenesis, ocular abnormalities

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            Multi-institutional survey of the aicardi syndrome in Japan

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              Aicardi Syndrome: A Longitudinal Clinical and Electroencephalographic Study

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                Author and article information

                Journal
                anp
                Arquivos de Neuro-Psiquiatria
                Arq. Neuro-Psiquiatr.
                Academia Brasileira de Neurologia - ABNEURO (São Paulo, SP, Brazil )
                0004-282X
                1678-4227
                June 2001
                : 59
                : 2B
                : 457-460
                Affiliations
                [02] orgnameFaculdade de Medicina Rio Preto orgdiv1Disciplina de Neurofisiologia Clínica
                [01] São José do Rio Preto SP orgnameFaculdade de Medicina Rio Preto orgdiv1Serviço de Neurologia Infantil Brasil
                Article
                S0004-282X2001000300029 S0004-282X(01)05900229
                6f6c2b28-c49f-4083-8c22-a5f7b5cdf137

                This work is licensed under a Creative Commons Attribution 4.0 International License.

                History
                : 14 September 2000
                : 12 January 2001
                : 17 January 2001
                Page count
                Figures: 0, Tables: 0, Equations: 0, References: 11, Pages: 4
                Product

                SciELO Brazil

                Self URI: Texto completo somente em PDF (PT)

                Aicardi syndrome,epilepsia,síndrome de Aicardi,EEG,RM,epilepsy,MRI
                Aicardi syndrome, epilepsia, síndrome de Aicardi, EEG, RM, epilepsy, MRI

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