A Rare Case of Primary Spinal Primitive Neuroectodermal Tumor with Long-term Follow-up

ABSTRACT

Primary primitive neuroectodermal tumors (PNETs) of the spine are rare. There have been 108 reported cases in the literature. These are aggressive malignancies with poor survival rates even after surgery, chemotherapy, and radiation. Since this is a rare disease, there are no standard guidelines for the management of these malignancies. Long-term survival with these tumors is unusual. We report a case of a 47-year-old patient with a primary PNET with 12-year follow-up; this is the longest follow-up recorded in literature.