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      Pulmonary Artery Aneurysm as a Cause for Chest Pain in a Patient with Noonan’s Syndrome: A Case Report

      a , b


      S. Karger AG

      Noonan’s syndrome, Aneurysm, Chest pain, Pulmonary artery aneurysm

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          A pulmonary artery aneurysm is defined as pulmonary artery dilatation >4 cm. Pulmonary artery aneurysms are rare findings and are usually not associated with chest pain. This is the first report of a case of pulmonary artery aneurysm causing chest pain in a patient with Noonan’s syndrome. Chest X-ray showed cardiomegaly and a prominent main pulmonary artery segment and CT confirmed a pulmonary artery aneurysm with a pulmonary artery root measuring 5.6 cm. The patient underwent pulmonary valvuloplasty as well as pulmonary arterioplasty to repair the pulmonary artery aneurysm, and experienced subsequent relief of chest pain. In conclusion, pulmonary artery aneurysm is a rare complication in patients with Noonan’s syndrome and can be the cause of chest pain in such patients.

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          Most cited references 2

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          Hilar mass in a patient with chest pain.

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            Giant aneurysms of the sinuses of Valsalva and aortic regurgitation in a patient with Noonan's syndrome.

            Noonan's syndrome is one of the commonest hereditary syndromes with cardiac involvement. We report a rare presentation of this syndrome, associated with giant aneurysms of the left and non-coronary sinuses of Valsalva, resulting in symptomatic aortic valve regurgitation. The patient's clinical investigations and operative management are presented. Histological examination of aortic tissues offers insight into the pathogenesis of these complications.

              Author and article information

              S. Karger AG
              June 2008
              12 December 2007
              : 110
              : 4
              : 249-251
              Departments of aInternal Medicine and bCardiology, University of Maryland Medical System, Baltimore, Md., USA
              112408 Cardiology 2008;110:249–251
              © 2007 S. Karger AG, Basel

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              Page count
              Figures: 3, References: 6, Pages: 3
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